GABARAPL1

Chr 12

GABA type A receptor associated protein like 1

Also known as: APG8-LIKE, APG8L, ATG8, ATG8B, ATG8L, GEC1

The encoded protein facilitates autophagosome maturation and endoplasmic reticulum turnover during cellular stress, while also regulating cell-surface trafficking of certain receptors. Mutations cause autosomal recessive intellectual disability with seizures and microcephaly, typically presenting in early childhood. This gene is highly constrained against loss-of-function variants, indicating that complete loss of protein function is likely not tolerated.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
38
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.50
LOEUF
Mechanism
Clinical SummaryGABARAPL1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.84) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.50LOEUF
pLI 0.835
Z-score 2.26
OE 0.00 (0.000.50)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.19Z-score
OE missense 0.58 (0.440.76)
36 obs / 62.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.000.50)
00.351.4
Missense OE0.58 (0.440.76)
00.61.4
Synonymous OE1.11
01.21.6
LoF obs/exp: 0 / 5.9Missense obs/exp: 36 / 62.5Syn Z: -0.42

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GABARAPL1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC