GAB3

Chr X

GRB2 associated binding protein 3

The protein functions as a scaffolding/docking protein that facilitates macrophage differentiation and participates in growth factor and cytokine signaling pathways by binding SHP2 tyrosine phosphatase and GRB2 adapter protein. Loss-of-function mutations cause autosomal dominant neurodevelopmental disorders due to haploinsufficiency, as indicated by the high pLI score and low LOEUF score showing strong intolerance to protein-truncating variants.

Summary from RefSeq
Research Assistant →
0
Active trials
7
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.34
LOEUF· LoF intol.
Mechanism
Clinical SummaryGAB3
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.95). One damaged copy is likely sufficient to cause disease.
Some data sources returned errors (1)

ensembl: TimeoutError: The operation was aborted due to timeout

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.34LOEUF
pLI 0.954
Z-score 3.55
OE 0.11 (0.040.34)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
1.47Z-score
OE missense 0.72 (0.640.82)
161 obs / 222.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.11 (0.040.34)
00.351.4
Missense OE0.72 (0.640.82)
00.61.4
Synonymous OE0.88
01.21.6
LoF obs/exp: 2 / 18.5Missense obs/exp: 161 / 222.6Syn Z: 0.85

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

GAB3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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