FZD8

Chr 10

frizzled class receptor 8

Also known as: FZ-8, hFZ8

The FZD8 protein is a seven-transmembrane receptor for Wnt signaling proteins that activates the beta-catenin canonical pathway, which is essential for tissue morphogenesis and cellular polarity during development. Mutations cause autosomal dominant microcephaly, seizures, and developmental delay, with onset in infancy or early childhood. This gene is highly constrained against loss-of-function variants, indicating that such mutations are likely to be pathogenic.

Summary from RefSeq, UniProt
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0
Active trials
11
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.42
LOEUF
Mechanism
Clinical SummaryFZD8
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.79) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Missense constrained — critical functional residues
LoF Constraint
0.42LOEUF
pLI 0.790
Z-score 3.32
OE 0.16 (0.070.42)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
3.16Z-score
OE missense 0.53 (0.470.60)
189 obs / 357.4 exp
Constrained

Highly missense-constrained (top ~0.1%)

Observed / Expected Ratios
LoF OE0.16 (0.070.42)
00.351.4
Missense OE0.53 (0.470.60)
00.61.4
Synonymous OE1.35
01.21.6
LoF obs/exp: 3 / 18.3Missense obs/exp: 189 / 357.4Syn Z: -3.55

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FZD8 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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