FTCDNL1

Chr 2

formiminotransferase cyclodeaminase N-terminal like

Also known as: FONG

The protein is predicted to bind folic acid and function as a transferase within membrane-bound cellular organelles. Mutations in this gene have been associated with neurodevelopmental disorders, though the clinical phenotype and inheritance patterns are not well-established based on current data. This gene shows moderate tolerance to loss-of-function variants (pLI 0.41, LOEUF 0.93), suggesting haploinsufficiency may not be the primary disease mechanism.

OMIMResearchSummary from RefSeq
GOFmechanismLOEUF 0.93
Clinical SummaryFTCDNL1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.20) despite low pLI — interpret in context.
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ClinVar Variants
33 unique Pathogenic / Likely Pathogenic· 2 VUS of 37 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.93LOEUF
pLI 0.405
Z-score 1.68
OE 0.20 (0.070.93)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.23Z-score
OE missense 0.58 (0.450.76)
40 obs / 68.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.20 (0.070.93)
00.351.4
Missense OE0.58 (0.450.76)
00.61.4
Synonymous OE0.85
01.21.6
LoF obs/exp: 1 / 5.1Missense obs/exp: 40 / 68.8Syn Z: 0.62
DN
0.6163th %ile
GOF
0.72top 25%
LOF
0.4628th %ile

The highest-scoring mechanism for this gene is gain-of-function.

GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

37 submitted variants in ClinVar

Classification Summary

Pathogenic32
Likely Pathogenic1
VUS2
Likely Benign1
32
Pathogenic
1
Likely Pathogenic
2
VUS
1
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
32
Likely Pathogenic
1
VUS
2
Likely Benign
1
Benign
0
Total36

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

FTCDNL1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found