FSCN1

Chr 7

fascin actin-bundling protein 1

The FSCN1 protein organizes actin filaments into parallel bundles and is essential for cell motility, migration, and formation of cellular protrusions including filopodia. Mutations cause autosomal recessive retinal dystrophy with early childhood onset, affecting vision and retinal function. This gene is highly constrained against loss-of-function variants, indicating that complete loss of protein function is likely poorly tolerated.

OMIMResearchSummary from RefSeq, UniProt
LOFmechanismLOEUF 0.41
Clinical SummaryFSCN1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.87) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.41LOEUF
pLI 0.869
Z-score 3.17
OE 0.13 (0.050.41)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.98Z-score
OE missense 0.69 (0.620.77)
224 obs / 324.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.13 (0.050.41)
00.351.4
Missense OE0.69 (0.620.77)
00.61.4
Synonymous OE1.03
01.21.6
LoF obs/exp: 2 / 15.4Missense obs/exp: 224 / 324.5Syn Z: -0.25
DN
0.3991th %ile
GOF
0.4282th %ile
LOF
0.66top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.41

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FSCN1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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