FNBP1

Chr 9

formin binding protein 1

Also known as: FBP17

The protein coordinates membrane tubulation with actin cytoskeleton reorganization during clathrin-mediated endocytosis by binding lipids to promote membrane invagination and enhancing actin polymerization through WASL/N-WASP recruitment. Loss-of-function mutations cause autosomal dominant neurodevelopmental disorders with high constraint against loss-of-function variants (pLI 0.83, LOEUF 0.36). The pathogenic mechanism involves disrupted endocytic processes critical for neuronal function and development.

OMIMResearchSummary from RefSeq, UniProt, Mechanism
LOFmechanismLOEUF 0.36
Clinical SummaryFNBP1
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.83) — some intolerance to loss-of-function variants.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.36LOEUF
pLI 0.828
Z-score 4.54
OE 0.19 (0.110.36)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.02Z-score
OE missense 0.68 (0.610.77)
223 obs / 325.8 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.19 (0.110.36)
00.351.4
Missense OE0.68 (0.610.77)
00.61.4
Synonymous OE0.96
01.21.6
LoF obs/exp: 7 / 36.6Missense obs/exp: 223 / 325.8Syn Z: 0.33
DN
0.5180th %ile
GOF
0.4579th %ile
LOF
0.64top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.36

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FNBP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →