The protein acts as an actin nucleation factor that assembles and reorganizes the actin cytoskeleton, promotes nuclear actin filament formation in response to DNA damage, and protects against cellular stress by stabilizing cell cycle arrest pathways. Biallelic mutations cause autosomal recessive intellectual developmental disorder (MRT47). This gene is highly constrained against loss-of-function variants in the general population.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 0.271 OMIM phenotype
Clinical SummaryFMN2
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.27LOEUF
pLI 0.998
Z-score 6.11
OE 0.16 (0.100.27)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
0.32Z-score
OE missense 0.97 (0.921.03)
856 obs / 882.6 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.16 (0.100.27)
00.351.4
Missense OE0.97 (0.921.03)
00.61.4
Synonymous OE1.32
01.21.6
LoF obs/exp: 10 / 61.9Missense obs/exp: 856 / 882.6Syn Z: -4.80
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
strongFMN2-related nonsyndromic intellectual disabilityLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.3892th %ile
GOF
0.5071th %ile
LOF
0.68top 10%

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FMN2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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