FLG2

Chr 1AR

filaggrin 2

Also known as: IFPS, PSS6

The filaggrin-like protein encoded by this gene is upregulated by calcium, proteolyzed by calpain 1, and is involved in epithelial homeostasis. The encoded protein is required for proper cornification in skin, with defects in this gene being associated with skin diseases. This protein also has a function in skin barrier protection. In fact, in addition to providing a physical barrier, C-terminal fragments of this protein display antimicrobial activity against P. aeruginosa and E. coli. [provided by RefSeq, Jul 2020]

OMIMResearchGenerating clinical summary…
MultiplemechanismARLOEUF 1.921 OMIM phenotype
Clinical SummaryFLG2
Population Constraint (gnomAD)
Low constraint (pLI 0.02) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.92LOEUF
pLI 0.018
Z-score -0.43
OE 1.38 (0.441.92)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-1.19Z-score
OE missense 1.10 (1.051.15)
1260 obs / 1146.2 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?1.38 (0.441.92)
00.351.4
Missense OE?1.10 (1.051.15)
00.61.4
Synonymous OE?1.18
01.21.6
LoF obs/exp: 2 / 1.4Missense obs/exp: 1260 / 1146.2Syn Z: -3.04
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
strongFLG2-related peeling skin syndromeOTHERAR

This gene — mechanism propensity

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.79top 25%
GOF
0.6932th %ile
LOF
0.3356th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FLG2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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