FJX1

Chr 11

four-jointed box kinase 1

The protein acts as an inhibitor of dendrite extension and branching, though its exact function in humans remains unclear based on homology to Drosophila developmental genes. The gene is highly constrained against loss-of-function variation (pLI 0.94, LOEUF 0.33), but no established human disease associations have been reported to date.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
4
Pubs (1 yr)
12
P/LP submissions
0%
P/LP missense
0.33
LOEUF· LoF intol.
Mechanism
Clinical SummaryFJX1
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.94). One damaged copy is likely sufficient to cause disease.
📋
ClinVar Variants
12 unique Pathogenic / Likely Pathogenic· 76 VUS of 88 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.33LOEUF
pLI 0.944
Z-score 2.80
OE 0.00 (0.000.33)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
0.66Z-score
OE missense 0.87 (0.760.98)
167 obs / 192.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.00 (0.000.33)
00.351.4
Missense OE0.87 (0.760.98)
00.61.4
Synonymous OE1.08
01.21.6
LoF obs/exp: 0 / 9.1Missense obs/exp: 167 / 192.7Syn Z: -0.62

ClinVar Variant Classifications

88 submitted variants in ClinVar

Classification Summary

Pathogenic12
VUS76
12
Pathogenic
76
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
12
0
12
Likely Pathogenic
0
0
0
0
0
VUS
0
66
10
0
76
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total06622088

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

FJX1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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