FECH

Chr 18

ferrochelatase

Also known as: EPP, EPP1, FCE

The protein encoded by this gene is localized to the mitochondrion, where it catalyzes the insertion of the ferrous form of iron into protoporphyrin IX in the heme synthesis pathway. Mutations in this gene are associated with erythropoietic protoporphyria. Two transcript variants encoding different isoforms have been found for this gene. A pseudogene of this gene is found on chromosome 3.[provided by RefSeq, May 2010]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtProtoporphyria, erythropoietic, 1

Clinical highlights

Gene-disease validity (ClinGen)
protoporphyria, erythropoietic, 1 · ARDefinitivesufficient evidence for diagnostic panels
0
Active trials
51
Pubs (1 yr)
P/LP submissions
P/LP missense
0.62
LOEUF
Mechanism
📖
GeneReview available — FECH
Authoritative clinical overview · Recommended first read
Open GeneReview ↗
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.62LOEUF
pLI 0.003
Z-score 3.03
OE 0.35 (0.210.62)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.34Z-score
OE missense 0.75 (0.670.85)
175 obs / 232.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.35 (0.210.62)
00.351.4
Missense OE?0.75 (0.670.85)
00.61.4
Synonymous OE?0.91
01.21.6
LoF obs/exp: 9 / 25.5Missense obs/exp: 175 / 232.4Syn Z: 0.65

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FECH · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →