FARP1

Chr 13

FERM, ARH/RhoGEF and pleckstrin domain protein 1

Also known as: CDEP, FARP1-IT1, GLCC1, PLEKHC2, PPP1R75

The protein functions as a guanine nucleotide exchange factor for RAC1 and promotes dendritic growth, spine formation, and synapse development in neurons. Mutations cause autosomal recessive epilepsy with intellectual disability and behavioral abnormalities, typically presenting in early childhood. The gene is extremely intolerant to loss-of-function variants (pLI near 1.0), indicating that complete loss of protein function is likely pathogenic.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.51
Clinical SummaryFARP1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.51LOEUF
pLI 0.000
Z-score 4.55
OE 0.35 (0.240.51)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
0.84Z-score
OE missense 0.91 (0.850.97)
593 obs / 653.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.35 (0.240.51)
00.351.4
Missense OE0.91 (0.850.97)
00.61.4
Synonymous OE1.06
01.21.6
LoF obs/exp: 20 / 57.1Missense obs/exp: 593 / 653.1Syn Z: -0.77

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FARP1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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