FAN1

Chr 15AR

FANCD2 and FANCI associated nuclease 1

Also known as: KIAA1018, KMIN, MTMR15, hFAN1

This gene plays a role in DNA interstrand cross-link repair and encodes a protein with 5' flap endonuclease and 5'-3' exonuclease activity. Mutations in this gene cause karyomegalic interstitial nephritis. Alternatively spliced transcript variants encoding distinct isoforms have been described. [provided by RefSeq, Feb 2016]

GeneReviewsOMIMResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

Interstitial nephritis, karyomegalicMIM #614817
AR

Clinical highlights

Gene-disease validity (ClinGen)
hereditary nonpolyposis colon cancer · ADLimitednot for standalone diagnostic reporting2 gene-disease associations curated in total
0
Active trials
28
Pubs (1 yr)
P/LP submissions
P/LP missense
1.12
LOEUF
Mechanism
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GeneReview available — FAN1
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.12LOEUF
pLI 0.000
Z-score 0.88
OE 0.86 (0.671.12)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.05Z-score
OE missense 1.01 (0.941.08)
571 obs / 567.8 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.86 (0.671.12)
00.351.4
Missense OE?1.01 (0.941.08)
00.61.4
Synonymous OE?1.08
01.21.6
LoF obs/exp: 42 / 48.6Missense obs/exp: 571 / 567.8Syn Z: -0.89

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FAN1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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