FAM91A1

Chr 8

family with sequence similarity 91 member A1

The protein functions as a component of the WDR11 complex that facilitates golgin-mediated capture of AP-1 generated vesicles at the trans-Golgi network. This gene is highly constrained against loss-of-function variants (LOEUF 0.488), suggesting mutations would likely cause severe disease, though no specific clinical phenotypes have been established in humans yet.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
1
Pubs (1 yr)
50
P/LP submissions
0%
P/LP missense
0.49
LOEUF
Mechanism
Clinical SummaryFAM91A1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.32) despite low pLI — interpret in context.
📋
ClinVar Variants
50 unique Pathogenic / Likely Pathogenic· 86 VUS of 181 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.49LOEUF
pLI 0.000
Z-score 4.44
OE 0.32 (0.220.49)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.16Z-score
OE missense 0.71 (0.650.78)
312 obs / 439.7 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.32 (0.220.49)
00.351.4
Missense OE0.71 (0.650.78)
00.61.4
Synonymous OE0.86
01.21.6
LoF obs/exp: 16 / 49.8Missense obs/exp: 312 / 439.7Syn Z: 1.33

ClinVar Variant Classifications

181 submitted variants in ClinVar

Classification Summary

Pathogenic50
VUS86
Likely Benign4
Benign2
50
Pathogenic
86
VUS
4
Likely Benign
2
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
50
0
50
Likely Pathogenic
0
0
0
0
0
VUS
0
82
4
0
86
Likely Benign
0
4
0
0
4
Benign
0
1
1
0
2
Total087550142

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

FAM91A1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found