FAM89A

Chr 1

family with sequence similarity 89 member A

Also known as: C1orf153

The FAM89A protein function is not well characterized in the provided data. Based on the gene constraint metrics showing moderate tolerance to loss-of-function variants (pLI 0.26, LOEUF 1.32), pathogenic variants in this gene would not be expected to cause severe early-onset developmental disorders. No established disease associations or inheritance patterns are documented in the provided information.

MultiplemechanismLOEUF 1.32
Clinical SummaryFAM89A
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.29) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.32LOEUF
pLI 0.257
Z-score 1.23
OE 0.29 (0.101.32)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.24Z-score
OE missense 0.92 (0.751.13)
66 obs / 71.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.29 (0.101.32)
00.351.4
Missense OE0.92 (0.751.13)
00.61.4
Synonymous OE0.92
01.21.6
LoF obs/exp: 1 / 3.5Missense obs/exp: 66 / 71.7Syn Z: 0.35
DN
0.6455th %ile
GOF
0.6736th %ile
LOF
0.4528th %ile

This gene has evidence for multiple mechanisms of pathogenicity (gain-of-function and dominant-negative). Both the Badonyi & Marsh prediction and the broader genomic evidence point to gain-of-function as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

GOFprediction above median
DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FAM89A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC