FAM246C

Chr 22

family with sequence similarity 246 member C (gene/pseudogene)

I notice that you've provided the gene name FAM246C but haven't included the supporting data about protein function, associated diseases, inheritance patterns, or constraint metrics that your instructions specify I should use. Without this essential information about what the FAM246C protein does, what conditions result from mutations, and the inheritance pattern, I cannot write an accurate clinical summary following your strict requirements to use only the provided data. Could you please provide the clinical and functional information for FAM246C that should inform this summary?

Multiplemechanism
Clinical SummaryFAM246C
📋
ClinVar Variants
178 unique Pathogenic / Likely Pathogenic· 9 VUS of 187 total submissions
Some data sources returned errors (1)

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

DN
0.6454th %ile
GOF
0.6444th %ile
LOF
0.3551th %ile

This gene has evidence for multiple mechanisms of pathogenicity (dominant-negative and gain-of-function). Both the Badonyi & Marsh prediction and the broader genomic evidence point to dominant-negative as the predominant mechanism. Different variants in this gene may act through different mechanisms — interpret in context of the specific variant.

DNprediction above median
GOFprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

187 submitted variants in ClinVar

Classification Summary

Pathogenic178
VUS9
178
Pathogenic
9
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
178
Likely Pathogenic
0
VUS
9
Likely Benign
0
Benign
0
Total187

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

FAM246C · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 1 full-text resultsSearch PubTator3 ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found