FAM151A

Chr 1

family with sequence similarity 151 member A

Also known as: C1orf179

The protein is located in extracellular exosomes but its specific function is not well characterized. Mutations in this gene cause autosomal recessive cone-rod dystrophy, a progressive retinal degeneration affecting both cone and rod photoreceptors that typically begins in childhood or adolescence. The gene shows tolerance to loss-of-function variants (pLI near 0, LOEUF 1.5), consistent with the recessive inheritance pattern observed in retinal dystrophy cases.

ResearchSummary from RefSeq
LOEUF 1.50
Clinical SummaryFAM151A
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.50LOEUF
pLI 0.000
Z-score -0.28
OE 1.06 (0.771.50)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.19Z-score
OE missense 1.03 (0.941.12)
354 obs / 344.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.06 (0.771.50)
00.351.4
Missense OE1.03 (0.941.12)
00.61.4
Synonymous OE1.14
01.21.6
LoF obs/exp: 24 / 22.6Missense obs/exp: 354 / 344.3Syn Z: -1.36

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

FAM151A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found