FAAP20

Chr 1

FA core complex associated protein 20

Also known as: C1orf86, FP7162

The protein is a component of the Fanconi anemia complex that recognizes ubiquitin modifications at DNA interstrand cross-links and recruits other repair factors to promote DNA repair and translesion synthesis. Mutations cause Fanconi anemia, a disorder characterized by bone marrow failure, developmental abnormalities, and cancer predisposition with autosomal recessive inheritance. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.751), reflecting its essential role in DNA repair.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
1
Pubs (1 yr)
136
P/LP submissions
0%
P/LP missense
0.75
LOEUF
Mechanism
Clinical SummaryFAAP20
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.53) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
129 unique Pathogenic / Likely Pathogenic· 34 VUS of 187 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.75LOEUF
pLI 0.526
Z-score 1.96
OE 0.16 (0.060.75)
Moderately constrained

Typical tolerance to LoF variation

Missense Constraint
0.20Z-score
OE missense 0.95 (0.811.12)
102 obs / 107.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.16 (0.060.75)
00.351.4
Missense OE0.95 (0.811.12)
00.61.4
Synonymous OE1.14
01.21.6
LoF obs/exp: 1 / 6.3Missense obs/exp: 102 / 107.8Syn Z: -0.77

ClinVar Variant Classifications

187 submitted variants in ClinVar

Classification Summary

Pathogenic125
Likely Pathogenic4
VUS34
Likely Benign8
Benign1
125
Pathogenic
4
Likely Pathogenic
34
VUS
8
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
125
0
125
Likely Pathogenic
0
0
4
0
4
VUS
0
15
19
0
34
Likely Benign
0
7
0
1
8
Benign
0
0
0
1
1
Total0221482172

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

FAAP20 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗