EXOC2

Chr 6

exocyst complex component 2

Also known as: NEDFACH, SEC5, SEC5L1, Sec5p

The protein encoded by this gene is a component of the exocyst complex, a multi-protein complex essential for the polarized targeting of exocytic vesicles to specific docking sites on the plasma membrane. Though best characterized in yeast, the component proteins and the functions of the exocyst complex have been demonstrated to be highly conserved in higher eukaryotes. At least eight components of the exocyst complex, including this protein, are found to interact with the actin cytoskeletal remodeling and vesicle transport machinery. This interaction has been shown to mediate filopodia formation in fibroblasts. This protein has been shown to interact with the Ral subfamily of GTPases and thereby mediate exocytosis by tethering vesicles to the plasma membrane. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2012]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtNeurodevelopmental disorder with dysmorphic facies and cerebellar hypoplasia

Clinical highlights

Gene-disease validity (ClinGen)
complex neurodevelopmental disorder · ARLimitednot for standalone diagnostic reporting
0
Active trials
5
Pubs (1 yr)
P/LP submissions
P/LP missense
0.59
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint?
0.59LOEUF
pLI 0.000
Z-score 4.12
OE 0.42 (0.310.59)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint?
1.70Z-score
OE missense 0.79 (0.720.85)
393 obs / 499.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.42 (0.310.59)
00.351.4
Missense OE?0.79 (0.720.85)
00.61.4
Synonymous OE?1.02
01.21.6
LoF obs/exp: 25 / 59.2Missense obs/exp: 393 / 499.7Syn Z: -0.23

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

EXOC2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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