ETFBKMT

Chr 12

electron transfer flavoprotein subunit beta lysine methyltransferase

Also known as: C12orf72, ETFB-KMT, METTL20

Enables heat shock protein binding activity and protein-lysine N-methyltransferase activity. Involved in negative regulation of fatty acid beta-oxidation using acyl-CoA dehydrogenase. Located in mitochondrial matrix. Part of protein-containing complex. [provided by Alliance of Genome Resources, Jul 2025]

0
Active trials
1
Pubs (1 yr)
32
P/LP submissions
P/LP missense
1.76
LOEUF
DN
Mechanism· predicted
Clinical SummaryETFBKMT
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
32 unique Pathogenic / Likely Pathogenic· 4 VUS of 47 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.76LOEUF
pLI 0.000
Z-score -0.42
OE 1.14 (0.731.76)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.26Z-score
OE missense 0.94 (0.811.09)
127 obs / 135.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.14 (0.731.76)
00.351.4
Missense OE0.94 (0.811.09)
00.61.4
Synonymous OE0.83
01.21.6
LoF obs/exp: 12 / 10.5Missense obs/exp: 127 / 135.4Syn Z: 0.95
DN
0.6260th %ile
GOF
0.4973th %ile
LOF
0.3260th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

47 submitted variants in ClinVar

Classification Summary

Pathogenic29
Likely Pathogenic3
VUS4
Likely Benign2
29
Pathogenic
3
Likely Pathogenic
4
VUS
2
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
29
Likely Pathogenic
3
VUS
4
Likely Benign
2
Benign
0
Total38

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

ETFBKMT · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found