ERICH5

Chr 8

glutamate rich 5

Also known as: C8orf47

ERICH5 encodes a protein containing glutamate-rich and histidine-rich domains whose specific cellular function remains unclear. Mutations cause autosomal recessive intellectual disability with seizures and dysmorphic features, typically manifesting in early childhood. The gene shows high tolerance to loss-of-function variants in the general population, consistent with a recessive inheritance pattern.

0
Active trials
0
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.21
LOEUF
Mechanism
Clinical SummaryERICH5
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
Some data sources returned errors (1)

opentargets: TimeoutError: The operation was aborted due to timeout

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.21LOEUF
pLI 0.000
Z-score 1.03
OE 0.69 (0.421.21)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.15Z-score
OE missense 1.03 (0.921.16)
199 obs / 192.9 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.69 (0.421.21)
00.351.4
Missense OE1.03 (0.921.16)
00.61.4
Synonymous OE0.90
01.21.6
LoF obs/exp: 9 / 13.0Missense obs/exp: 199 / 192.9Syn Z: 0.64

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ERICH5 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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