EMG1

Chr 12

EMG1 N1-specific pseudouridine methyltransferase

Also known as: C2F, Grcc2f, NEP1

This gene encodes an essential, conserved eukaryotic protein that methylates pseudouridine in 18S rRNA. The related protein in yeast is a component of the small subunit processome and is essential for biogenesis of the ribosomal 40S subunit. A mutation in this gene has been associated with Bowen-Conradi syndrome. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Feb 2016]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtBowen-Conradi syndrome

Clinical highlights

Gene-disease validity (ClinGen)
Bowen-Conradi syndrome · ARStrongappropriate for clinical testing
0
Active trials
10
Pubs (1 yr)
P/LP submissions
P/LP missense
1.25
LOEUF
DN
Mechanism· predicted
📖
GeneReview available — EMG1
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
1.25LOEUF
pLI 0.000
Z-score 0.94
OE 0.71 (0.431.25)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint?
-0.30Z-score
OE missense 1.07 (0.941.23)
147 obs / 137.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios?
LoF OE?0.71 (0.431.25)
00.351.4
Missense OE?1.07 (0.941.23)
00.61.4
Synonymous OE?1.28
01.21.6
LoF obs/exp: 9 / 12.6Missense obs/exp: 147 / 137.0Syn Z: -1.56

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

EMG1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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