ELP2

Chr 18AR

elongator acetyltransferase complex subunit 2

Also known as: MRT58, SHINC-2, STATIP1, StIP

ELP2 encodes a core subunit of the elongator complex, which catalyzes essential tRNA modifications including carboxymethyluridine formation at the wobble base position and functions as a histone acetyltransferase that associates with RNA polymerase II for transcriptional elongation. Biallelic mutations cause autosomal recessive intellectual developmental disorder. This represents a relatively recently described cause of intellectual disability involving defects in tRNA modification pathways.

OMIMResearchSummary from RefSeq, OMIM, UniProt
ARLOEUF 0.881 OMIM phenotype
Clinical SummaryELP2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.88LOEUF
pLI 0.000
Z-score 2.30
OE 0.68 (0.530.88)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.58Z-score
OE missense 0.92 (0.851.00)
419 obs / 453.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.68 (0.530.88)
00.351.4
Missense OE0.92 (0.851.00)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 40 / 59.1Missense obs/exp: 419 / 453.5Syn Z: 0.02

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ELP2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC