EIF5A

Chr 17AD

eukaryotic translation initiation factor 5A

Also known as: EIF-5A, EIF5A1, FABAS, eIF-4D, eIF5AI

EIF5A encodes a translation factor that promotes ribosome rescue when stalled at specific amino acid sequences, particularly polyproline motifs, and regulates apoptosis and autophagy. Mutations cause Faundes-Banka syndrome with autosomal dominant inheritance. The gene shows moderate constraint against loss-of-function variants (LOEUF 0.543), suggesting intolerance to complete protein loss.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismADLOEUF 0.541 OMIM phenotype
Clinical SummaryEIF5A
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.74) — some intolerance to loss-of-function variants.
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ClinVar Variants
43 unique Pathogenic / Likely Pathogenic· 28 VUS of 89 total submissions
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Clinical Trials
2 active or recruiting trials — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.54LOEUF
pLI 0.737
Z-score 2.43
OE 0.11 (0.040.54)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.41Z-score
OE missense 0.34 (0.260.45)
35 obs / 104.1 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.11 (0.040.54)
00.351.4
Missense OE0.34 (0.260.45)
00.61.4
Synonymous OE1.36
01.21.6
LoF obs/exp: 1 / 8.7Missense obs/exp: 35 / 104.1Syn Z: -1.83

ClinVar Variant Classifications

89 submitted variants in ClinVar

Classification Summary

Pathogenic31
Likely Pathogenic12
VUS28
Likely Benign6
Benign1
31
Pathogenic
12
Likely Pathogenic
28
VUS
6
Likely Benign
1
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
2
3
26
0
31
Likely Pathogenic
5
4
3
0
12
VUS
3
18
7
0
28
Likely Benign
0
1
1
4
6
Benign
0
0
1
0
1
Total102638478

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

EIF5A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold
Clinical Literature
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