EIF4E3

Chr 3

eukaryotic translation initiation factor 4E family member 3

Also known as: eIF-4E3, eIF4E-3

EIF4E3 encodes a translation initiation factor that recognizes and binds the 7-methylguanosine cap of mRNA during protein synthesis initiation and may inhibit EIF4E1 activity. Mutations cause intellectual developmental disorder with seizures and language delay, inherited in an autosomal recessive pattern. The gene is not highly constrained against loss-of-function variants, consistent with the recessive inheritance pattern observed in affected individuals.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
9
Pubs (1 yr)
15
P/LP submissions
0%
P/LP missense
0.81
LOEUF
Mechanism
Clinical SummaryEIF4E3
Population Constraint (gnomAD)
Low constraint (pLI 0.02) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
15 unique Pathogenic / Likely Pathogenic· 74 VUS of 103 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.81LOEUF
pLI 0.018
Z-score 2.05
OE 0.39 (0.200.81)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.51Z-score
OE missense 0.85 (0.711.03)
78 obs / 91.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.39 (0.200.81)
00.351.4
Missense OE0.85 (0.711.03)
00.61.4
Synonymous OE0.99
01.21.6
LoF obs/exp: 5 / 13.0Missense obs/exp: 78 / 91.8Syn Z: 0.03

ClinVar Variant Classifications

103 submitted variants in ClinVar

Classification Summary

Pathogenic14
Likely Pathogenic1
VUS74
14
Pathogenic
1
Likely Pathogenic
74
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
14
0
14
Likely Pathogenic
0
0
1
0
1
VUS
0
67
7
0
74
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total06722089

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

EIF4E3 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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