EIF2B1

Chr 12

eukaryotic translation initiation factor 2B subunit alpha

Also known as: EIF2B, EIF2BA, EIF2Balpha, VWM1

This gene encodes one of five subunits of eukaryotic translation initiation factor 2B (EIF2B), a GTP exchange factor for eukaryotic initiation factor 2 and an essential regulator for protein synthesis. Mutations in this gene and the genes encoding other EIF2B subunits have been associated with leukoencephalopathy with vanishing white matter. [provided by RefSeq, Oct 2009]

GeneReviewsResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtLeukoencephalopathy with vanishing white matter 1

Clinical highlights

Gene-disease validity (ClinGen)
leukoencephalopathy with vanishing white matter 1 · ARDefinitivesufficient evidence for diagnostic panels
0
Active trials
13
Pubs (1 yr)
P/LP submissions
P/LP missense
0.98
LOEUF
DN
Mechanism· predicted
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GeneReview available — EIF2B1
Authoritative clinical overview · Recommended first read
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Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.98LOEUF
pLI 0.000
Z-score 1.64
OE 0.56 (0.340.98)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
1.38Z-score
OE missense 0.70 (0.600.81)
114 obs / 163.7 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios?
LoF OE?0.56 (0.340.98)
00.351.4
Missense OE?0.70 (0.600.81)
00.61.4
Synonymous OE?1.10
01.21.6
LoF obs/exp: 9 / 16.1Missense obs/exp: 114 / 163.7Syn Z: -0.61

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

EIF2B1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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