EIF1AX

Chr X

eukaryotic translation initiation factor 1A X-linked

Also known as: EIF1A, EIF1AP1, EIF4C, eIF-1A, eIF-4C

This gene encodes eukaryotic translation initiation factor 1A-X, an essential protein required for ribosome binding to mRNA and start codon recognition during protein synthesis. Mutations cause X-linked intellectual disability with variable features including developmental delay, seizures, and growth abnormalities. The gene is highly constrained against loss-of-function variants, and inheritance follows an X-linked pattern.

Summary from RefSeq, UniProt
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0
Active trials
26
Pubs (1 yr)
0
P/LP submissions
P/LP missense
0.39
LOEUF
LOF
Mechanism· predicted
Clinical SummaryEIF1AX
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 0.91). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

LoF intolerant — likely haploinsufficient
LoF Constraint
0.39LOEUF
pLI 0.910
Z-score 2.58
OE 0.00 (0.000.39)
Highly constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.39Z-score
OE missense 0.08 (0.040.17)
4 obs / 53.0 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.00 (0.000.39)
00.351.4
Missense OE0.08 (0.040.17)
00.61.4
Synonymous OE0.86
01.21.6
LoF obs/exp: 0 / 7.8Missense obs/exp: 4 / 53.0Syn Z: 0.48
DN
0.4587th %ile
GOF
0.3788th %ile
LOF
0.72top 10%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.39

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

EIF1AX · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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