EI24

Chr 11

EI24 autophagy associated transmembrane protein

Also known as: EPG4, PIG8, TP53I8

This gene encodes a tumor suppressor protein that acts as a negative growth regulator through the p53-mediated apoptosis pathway and regulates formation of degradative autolysosomes during autophagy. The gene is highly constrained against loss-of-function variation, but pathogenic variants and associated clinical phenotypes have not yet been established in pediatric patients. Further research is needed to determine if EI24 mutations cause recognizable neurodevelopmental or neurological disorders in children.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
8
Pubs (1 yr)
62
P/LP submissions
2%
P/LP missense
0.42
LOEUF
Mechanism
Clinical SummaryEI24
Population Constraint (gnomAD)
Moderately constrained gene (pLI 0.73) — some intolerance to loss-of-function variants.
📋
ClinVar Variants
62 unique Pathogenic / Likely Pathogenic· 23 VUS of 102 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.42LOEUF
pLI 0.733
Z-score 3.54
OE 0.18 (0.090.42)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.00Z-score
OE missense 0.58 (0.500.68)
105 obs / 180.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.18 (0.090.42)
00.351.4
Missense OE0.58 (0.500.68)
00.61.4
Synonymous OE0.65
01.21.6
LoF obs/exp: 4 / 21.9Missense obs/exp: 105 / 180.5Syn Z: 2.20

ClinVar Variant Classifications

102 submitted variants in ClinVar

Classification Summary

Pathogenic59
Likely Pathogenic3
VUS23
59
Pathogenic
3
Likely Pathogenic
23
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
59
0
59
Likely Pathogenic
0
1
2
0
3
VUS
0
19
4
0
23
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total02065085

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

EI24 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →