EEF2K

Chr 16

eukaryotic elongation factor 2 kinase

Also known as: CaMKIII, HSU93850, eEF-2K

This gene encodes eukaryotic elongation factor 2 kinase, a threonine kinase that regulates protein synthesis by phosphorylating elongation factor EEF2 and rendering it unable to bind ribosomes. Mutations cause neurodevelopmental disorder with seizures and nystagmus, inherited in an autosomal recessive pattern. The gene is extremely intolerant to loss-of-function variants, indicating that complete loss of function is likely incompatible with normal development.

GeneReviewsOMIMResearchSummary from RefSeq, UniProt
LOEUF 1.08
Clinical SummaryEEF2K
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
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GeneReview available — EEF2K
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.08LOEUF
pLI 0.000
Z-score 1.13
OE 0.81 (0.621.08)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.61Z-score
OE missense 0.92 (0.851.00)
432 obs / 469.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.81 (0.621.08)
00.351.4
Missense OE0.92 (0.851.00)
00.61.4
Synonymous OE0.97
01.21.6
LoF obs/exp: 34 / 41.9Missense obs/exp: 432 / 469.4Syn Z: 0.33

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

EEF2K · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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