EEF2

Chr 19AD

eukaryotic translation elongation factor 2

Also known as: EEF-2, EF-2, EF2, SCA26

This protein catalyzes the GTP-dependent ribosomal translocation step during translation elongation, moving tRNA molecules and mRNA through the ribosome during protein synthesis. Mutations cause spinocerebellar ataxia 26, inherited in an autosomal dominant pattern. The gene is highly constrained against loss-of-function variants (pLI 1.0, LOEUF 0.17), reflecting the essential nature of this translation factor.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismADLOEUF 0.171 OMIM phenotype
Clinical SummaryEEF2
Population Constraint (gnomAD)
Highly constrained gene — heterozygous loss-of-function variants are very rare in the population (pLI 1.00). One damaged copy is likely sufficient to cause disease.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Dual constrained — LoF & missense intolerant
LoF Constraint
0.17LOEUF
pLI 1.000
Z-score 5.31
OE 0.05 (0.020.17)
Highly constrained

Highly LoF-intolerant (top ~10% of genes)

Missense Constraint
4.88Z-score
OE missense 0.42 (0.380.47)
235 obs / 559.8 exp
Constrained

Highly missense-constrained (top ~0.1%)

Observed / Expected Ratios
LoF OE0.05 (0.020.17)
00.351.4
Missense OE0.42 (0.380.47)
00.61.4
Synonymous OE1.53
01.21.6
LoF obs/exp: 2 / 36.7Missense obs/exp: 235 / 559.8Syn Z: -6.67
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedEEF2-related developmental disorderLOFAD
DN
0.4190th %ile
GOF
0.4973th %ile
LOF
0.67top 25%

The highest-scoring mechanism for this gene is loss-of-function (haploinsufficiency).

LOFprediction above median · LOEUF 0.17

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312. Mechanism ranking also informed by gnomAD constraint, ClinVar, and ClinGen data.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

EEF2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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