EDRF1

Chr 10

erythroid differentiation regulatory factor 1

Also known as: C10orf137

EDRF1 encodes a transcription factor that regulates erythroid differentiation and globin gene expression by inhibiting DNA binding of GATA-1. Mutations cause erythropoietic protoporphyria with severe hemolytic anemia, an autosomal recessive disorder affecting red blood cell production and leading to significant anemia. The gene is highly constrained against loss-of-function variants (LOEUF 0.402), indicating that complete loss of function is likely deleterious.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.40
Clinical SummaryEDRF1
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.27) despite low pLI — interpret in context.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.40LOEUF
pLI 0.004
Z-score 5.50
OE 0.27 (0.190.40)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
2.70Z-score
OE missense 0.70 (0.650.76)
452 obs / 645.1 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios
LoF OE0.27 (0.190.40)
00.351.4
Missense OE0.70 (0.650.76)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 18 / 66.4Missense obs/exp: 452 / 645.1Syn Z: 0.03

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

EDRF1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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