ECM2

Chr 9

extracellular matrix protein 2

Extracellular matrix protein 2 promotes matrix assembly and cell adhesiveness in the extracellular space. This gene is not highly constrained against loss-of-function variants and currently has no established disease associations in pediatric neurology. The protein's role in extracellular matrix organization suggests potential involvement in developmental or structural processes, but pathogenic variants have not been definitively linked to human disease.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 0.92
Clinical SummaryECM2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.92LOEUF
pLI 0.000
Z-score 1.88
OE 0.62 (0.430.92)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.70Z-score
OE missense 0.90 (0.820.98)
328 obs / 365.5 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.62 (0.430.92)
00.351.4
Missense OE0.90 (0.820.98)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 18 / 28.9Missense obs/exp: 328 / 365.5Syn Z: 0.02
DN
0.7130th %ile
GOF
0.5465th %ile
LOF
0.3261th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

ECM2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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