DZANK1

Chr 20

double zinc ribbon and ankyrin repeat domains 1

Also known as: ANKRD64, C20orf12, C20orf84

The DZANK1 protein contains ankyrin repeat domains that mediate protein-protein interactions and is involved in vesicle transport in photoreceptor cells. Mutations cause autosomal recessive retinal dystrophy with early childhood onset, leading to progressive vision loss. This gene is not highly constrained against loss-of-function variants.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
0
Pubs (1 yr)
23
P/LP submissions
0%
P/LP missense
1.17
LOEUF
Mechanism
Clinical SummaryDZANK1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
23 unique Pathogenic / Likely Pathogenic· 110 VUS of 163 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.17LOEUF
pLI 0.000
Z-score 0.71
OE 0.88 (0.671.17)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.14Z-score
OE missense 1.02 (0.941.11)
395 obs / 387.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.88 (0.671.17)
00.351.4
Missense OE1.02 (0.941.11)
00.61.4
Synonymous OE0.99
01.21.6
LoF obs/exp: 34 / 38.8Missense obs/exp: 395 / 387.5Syn Z: 0.11

ClinVar Variant Classifications

163 submitted variants in ClinVar

Classification Summary

Pathogenic23
VUS110
Likely Benign4
23
Pathogenic
110
VUS
4
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
23
0
23
Likely Pathogenic
0
0
0
0
0
VUS
0
106
4
0
110
Likely Benign
0
4
0
0
4
Benign
0
0
0
0
0
Total0110270137

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

DZANK1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC