DYNLT2B

Chr 3AR

dynein light chain Tctex-type 2B

Also known as: SRTD17, TCTEX1D2

Dyneins are a group of microtubule-activated ATPases that function as molecular motors. They are divided into two subgroups of axonemal and cytoplasmic dyneins. The cytoplasmic dyneins function in intracellular motility, including retrograde axonal transport, protein sorting, organelle movement, and spindle dynamics. Molecules of conventional cytoplasmic dynein are comprised of 2 heavy chain polypeptides and a number of intermediate and light chains. This gene encodes a subunit of the human cytoplasmic dynein-2 complex. Mutations in this gene are associated with short-rib thoracic dysplasia 17 with or without polydactyly. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, May 2017]

Primary Disease Associations & Inheritance

Short-rib thoracic dysplasia 17 with or without polydactylyMIM #617405
AR
0
Active trials
1
Pubs (1 yr)
0
P/LP submissions
P/LP missense
1.49
LOEUF
DN
Mechanism· predicted
Clinical SummaryDYNLT2B
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.49LOEUF
pLI 0.000
Z-score 0.61
OE 0.76 (0.421.49)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.01Z-score
OE missense 0.67 (0.530.85)
48 obs / 72.0 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.76 (0.421.49)
00.351.4
Missense OE0.67 (0.530.85)
00.61.4
Synonymous OE0.82
01.21.6
LoF obs/exp: 6 / 7.9Missense obs/exp: 48 / 72.0Syn Z: 0.70
DN
0.6454th %ile
GOF
0.5563th %ile
LOF
0.4431th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

DYNLT2B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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