DTD1

Chr 20

D-aminoacyl-tRNA deacylase 1

Also known as: C20orf88, DTD, DUE-B, DUEB, HARS2, pqn-68

The protein encoded by DTD1 functions as a possible ATPase involved in DNA replication and may facilitate loading of CDC45 onto pre-replication complexes. Mutations cause autosomal recessive intellectual disability with seizures and hypotonia. This gene is not highly constrained against loss-of-function variants.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
1
Pubs (1 yr)
24
P/LP submissions
0%
P/LP missense
1.04
LOEUF
Mechanism
Clinical SummaryDTD1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
24 unique Pathogenic / Likely Pathogenic· 25 VUS of 52 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.04LOEUF
pLI 0.002
Z-score 1.48
OE 0.53 (0.291.04)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
1.18Z-score
OE missense 0.69 (0.580.83)
81 obs / 116.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.53 (0.291.04)
00.351.4
Missense OE0.69 (0.580.83)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 6 / 11.4Missense obs/exp: 81 / 116.8Syn Z: -0.11

ClinVar Variant Classifications

52 submitted variants in ClinVar

Classification Summary

Pathogenic23
Likely Pathogenic1
VUS25
23
Pathogenic
1
Likely Pathogenic
25
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
23
0
23
Likely Pathogenic
0
0
1
0
1
VUS
0
23
2
0
25
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total02326049

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

DTD1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗