DRC11

Chr 2

dynein regulatory complex subunit 11

Also known as: 4930465P12Rik, IQCA, IQCA1

The encoded protein is a component of the nexin-dynein regulatory complex that regulates ciliary and flagellar motility by maintaining axoneme alignment and controlling microtubule sliding. Mutations cause primary ciliary dyskinesia, a disorder affecting the respiratory system, fertility, and often leading to organ laterality defects. Primary ciliary dyskinesia follows autosomal recessive inheritance.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
1
Pubs (1 yr)
64
P/LP submissions
0%
P/LP missense
LOEUF
Mechanism
Clinical SummaryDRC11
📋
ClinVar Variants
64 unique Pathogenic / Likely Pathogenic· 51 VUS of 139 total submissions
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/DRC11?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

139 submitted variants in ClinVar

Classification Summary

Pathogenic63
Likely Pathogenic1
VUS51
Likely Benign3
63
Pathogenic
1
Likely Pathogenic
51
VUS
3
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
63
0
63
Likely Pathogenic
0
0
1
0
1
VUS
0
46
5
0
51
Likely Benign
0
3
0
0
3
Benign
0
0
0
0
0
Total049690118

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

DRC11 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
The Genetic Defects of N-DRC in Male Infertility.
Qin J et al.·Clin Genet
2026Review
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found