DPPA4

Chr 3

developmental pluripotency associated 4

Also known as: 2410091M23Rik

The DPPA4 protein is a nuclear factor that maintains pluripotency in stem cells and modifies chromatin through its DNA-binding SAP domain, playing an essential role in embryogenesis. Mutations cause a severe developmental disorder with skeletal and lung abnormalities that typically results in late embryonic or early neonatal lethality. The gene shows very low constraint against loss-of-function variants, consistent with the early lethal phenotype observed in mouse models.

OMIMResearchSummary from RefSeq, UniProt
LOEUF 0.95
Clinical SummaryDPPA4
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.95LOEUF
pLI 0.000
Z-score 1.72
OE 0.53 (0.310.95)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
0.34Z-score
OE missense 0.92 (0.811.06)
150 obs / 162.3 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.53 (0.310.95)
00.351.4
Missense OE0.92 (0.811.06)
00.61.4
Synonymous OE1.25
01.21.6
LoF obs/exp: 8 / 15.2Missense obs/exp: 150 / 162.3Syn Z: -1.54

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

DPPA4 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC