DNASE2B

Chr 1

deoxyribonuclease 2 beta

Also known as: DLAD

The protein functions as an endonuclease that hydrolyzes DNA under acidic conditions without requiring divalent cations, with expression restricted to salivary glands and lungs, and participates in nuclear DNA degradation during lens cell differentiation. This gene is extremely tolerant of loss-of-function variants (pLI near zero), and no established Mendelian diseases have been definitively linked to DNASE2B mutations in current medical literature.

Summary from RefSeq, UniProt
Research Assistant →
0
Active trials
5
Pubs (1 yr)
16
P/LP submissions
0%
P/LP missense
1.63
LOEUF
Mechanism
Clinical SummaryDNASE2B
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
16 unique Pathogenic / Likely Pathogenic· 37 VUS of 55 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.63LOEUF
pLI 0.000
Z-score -0.61
OE 1.15 (0.821.63)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.16Z-score
OE missense 0.97 (0.851.10)
172 obs / 177.8 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.15 (0.821.63)
00.351.4
Missense OE0.97 (0.851.10)
00.61.4
Synonymous OE1.07
01.21.6
LoF obs/exp: 22 / 19.1Missense obs/exp: 172 / 177.8Syn Z: -0.42

ClinVar Variant Classifications

55 submitted variants in ClinVar

Classification Summary

Pathogenic14
Likely Pathogenic2
VUS37
14
Pathogenic
2
Likely Pathogenic
37
VUS

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
14
0
14
Likely Pathogenic
0
0
2
0
2
VUS
0
34
3
0
37
Likely Benign
0
0
0
0
0
Benign
0
0
0
0
0
Total03419053

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

DNASE2B · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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