DNAAF11

Chr 8AR

dynein axonemal assembly factor 11

Also known as: CILD19, LRRC6, LRTP, TSLRP, tilB

The protein is involved in dynein arm assembly and transports outer dynein arm proteins from the cytoplasm to cilia, making it crucial for ciliary motility and sperm flagella formation. Mutations cause primary ciliary dyskinesia-19, a condition affecting respiratory function, fertility, and organ positioning due to defective ciliary motility. This follows autosomal recessive inheritance.

OMIMResearchSummary from RefSeq, OMIM, UniProt
LOFmechanismARLOEUF 1.081 OMIM phenotype
Clinical SummaryDNAAF11
🧬
Gene-Disease Validity (ClinGen)
primary ciliary dyskinesia 19 · ARDefinitive

Definitive — sufficient evidence for diagnostic panels

Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
💊
Clinical Trials
8 active or recruiting trials — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.08LOEUF
pLI 0.000
Z-score 1.23
OE 0.74 (0.511.08)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.13Z-score
OE missense 1.02 (0.921.14)
243 obs / 237.4 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.74 (0.511.08)
00.351.4
Missense OE1.02 (0.921.14)
00.61.4
Synonymous OE1.02
01.21.6
LoF obs/exp: 19 / 25.7Missense obs/exp: 243 / 237.4Syn Z: -0.14
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
definitiveDNAAF11-related primary ciliary dyskinesiaLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.7130th %ile
GOF
0.6540th %ile
LOF
0.2386th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

DNAAF11 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

Porphyria, Acute Intermittent

Clinical Research on Acute Intermittent Porphyria and the Use of Carbohydrate-Rich Diet as a Treatment

RECRUITING
NCT06273644Phase NANordlandssykehuset HFStarted 2024-01-27
Carbohydrates
Transgender Individuals

Effects of Gender-Affirming Hormone Therapy on Cardiovascular, Metabolic, and Mental Health Outcomes in Transgender Adults.

NOT YET RECRUITING
NCT07394400Milagros Rocha BarajasStarted 2026-02-14
Endometriosis

" Development of Primary Cultures of Diaphragmatic Myoblasts for Basic Research Purposes "

NOT YET RECRUITING
NCT07380308Assistance Publique - Hôpitaux de ParisStarted 2026-02-01
During the surgery planned as part of the routine care of the patient, a part of the tissue sample will be saved in order to carry out the analysis planned for the research.
CystinosisNative Kidney

Cystinosis and Mitochondrial Metabolism

NOT YET RECRUITING
NCT07319091Phase NAHospices Civils de LyonStarted 2026-01
Mitochondrial metabolism
Melanoma

Evolution of Metabolic and Immune Dysfunction in In-transit Melanoma

RECRUITING
NCT04658303Yana NajjarStarted 2021-02-24
Pimonidazole
Female Infertility

Female Fertility, Environmental Agents and Stress Oxidant

RECRUITING
NCT04866329University Hospital, ToursStarted 2021-12-08
Blood sampleUrine sampleFollicular fluid and granulosa cells sample
VaccinationImmunosenescenceMetabolism

VITAL: Vaccination, Immunity, Time-restricted Eating, Aging and Lifestyle

RECRUITING
NCT07000708Phase NACharite University, Berlin, GermanyStarted 2025-09-10
TRE: Time-restricted eating
Rectal Cancer PatientsObesity &Amp; OverweightLocally Advanced Rectal Cancer (LARC)

Evaluating the Impact of GLP-1 Receptor Agonists With Total Neoadjuvant Therapy in Rectal Cancer

NOT YET RECRUITING
NCT07314528Phase PHASE2St. James's Hospital, IrelandStarted 2026-04
GLP-1 receptor agonistTotal neoadjuvant therapy (TNT)
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found