DIPK1C

Chr 18

divergent protein kinase domain 1C

Also known as: C18orf51, FAM69C, FNCAD

The protein is a cysteine-rich transmembrane protein that localizes to the endoplasmic reticulum, though its specific function remains unknown. Mutations cause autosomal recessive developmental and epileptic encephalopathy with microcephaly. This gene is not highly constrained against loss-of-function variants.

Summary from RefSeq
Research Assistant →
0
Active trials
0
Pubs (1 yr)
153
P/LP submissions
0%
P/LP missense
1.82
LOEUF
Mechanism
Clinical SummaryDIPK1C
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
151 unique Pathogenic / Likely Pathogenic· 111 VUS of 276 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.82LOEUF
pLI 0.000
Z-score -0.39
OE 1.15 (0.691.82)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.04Z-score
OE missense 1.01 (0.901.14)
195 obs / 193.3 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE1.15 (0.691.82)
00.351.4
Missense OE1.01 (0.901.14)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 9 / 7.8Missense obs/exp: 195 / 193.3Syn Z: 0.48

ClinVar Variant Classifications

276 submitted variants in ClinVar

Classification Summary

Pathogenic145
Likely Pathogenic6
VUS111
Likely Benign12
145
Pathogenic
6
Likely Pathogenic
111
VUS
12
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
145
0
145
Likely Pathogenic
0
0
6
0
6
VUS
0
91
20
0
111
Likely Benign
0
9
2
1
12
Benign
0
0
0
0
0
Total01001731274

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

DIPK1C · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found