DHX32

Chr 10

DEAH-box helicase 32 (putative)

Also known as: DDX32, DHLP1

The protein is a DEAD box RNA helicase involved in cellular processes that alter RNA secondary structure including translation initiation, nuclear and mitochondrial splicing, and ribosome assembly. Mutations in DHX32 cause autosomal recessive neurodevelopmental disorder with seizures, hypotonia, and brain abnormalities. This gene shows minimal constraint against loss-of-function variants, consistent with recessive inheritance where heterozygous carriers are typically unaffected.

OMIMResearchSummary from RefSeq
LOFmechanismLOEUF 0.89
Clinical SummaryDHX32
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
7 unique Pathogenic / Likely Pathogenic· 57 VUS of 100 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
0.89LOEUF
pLI 0.000
Z-score 2.05
OE 0.61 (0.420.89)
Tolerant

Typical tolerance to LoF variation

Missense Constraint
1.26Z-score
OE missense 0.82 (0.750.90)
331 obs / 402.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.61 (0.420.89)
00.351.4
Missense OE0.82 (0.750.90)
00.61.4
Synonymous OE1.00
01.21.6
LoF obs/exp: 19 / 31.4Missense obs/exp: 331 / 402.1Syn Z: -0.01
Curated Mechanism (G2P)Gene2Phenotype (DDG2P) ↗
limitedDHX32-related retinitis pigmentosaLOFAR

Predictions shown for reference only — model trained on dominant genes, not applicable to AR conditions.

DN
0.6260th %ile
GOF
0.5072th %ile
LOF
0.3355th %ile

The Badonyi & Marsh prediction model was trained exclusively on dominant disease genes. Predictions are not reliable for genes with autosomal recessive inheritance and are shown at reduced opacity for reference only.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

100 submitted variants in ClinVar

Classification Summary

Pathogenic7
VUS57
Likely Benign36
7
Pathogenic
57
VUS
36
Likely Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
7
0
7
Likely Pathogenic
0
0
0
0
0
VUS
7
46
3
1
57
Likely Benign
0
2
12
22
36
Benign
0
0
0
0
0
Total7482223100

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

DHX32 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Open Research Assistant →
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC