DHX16

Chr 6

DEAH-box helicase 16

Also known as: DBP2, DDX16, NMOAS, PRO2014, PRP8, PRPF2, Prp2

DEAD box proteins, characterized by the conserved motif Asp-Glu-Ala-Asp (DEAD), are putative RNA helicases. They are implicated in a number of cellular processes involving alteration of RNA secondary structure such as translation initiation, nuclear and mitochondrial splicing, and ribosome and spliceosome assembly. Based on their distribution patterns, some members of this family are believed to be involved in embryogenesis, spermatogenesis, and cellular growth and division. This gene encodes a DEAD box protein, which is a functional homolog of fission yeast Prp8 protein involved in cell cycle progression. This gene is mapped to the MHC region on chromosome 6p21.3, a region where many malignant, genetic and autoimmune disease genes are linked. Three transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, May 2018]

ResearchGenerating clinical summary…

Primary Disease Associations & Inheritance

UniProtNeuromuscular oculoauditory syndrome
0
Active trials
8
Pubs (1 yr)
P/LP submissions
P/LP missense
0.64
LOEUF
DN
Mechanism· predicted
Some data sources returned errors (1)

omim: Error: OMIM fetch failed: 429

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint?
0.64LOEUF
pLI 0.000
Z-score 3.96
OE 0.47 (0.350.64)
Tolerant

Typical tolerance to LoF variation

Missense Constraint?
3.08Z-score
OE missense 0.66 (0.600.71)
417 obs / 635.4 exp
Mild constraint

Moderately missense-constrained (top ~2.5%)

Observed / Expected Ratios?
LoF OE?0.47 (0.350.64)
00.351.4
Missense OE?0.66 (0.600.71)
00.61.4
Synonymous OE?0.88
01.21.6
LoF obs/exp: 31 / 65.6Missense obs/exp: 417 / 635.4Syn Z: 1.47

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

DHX16 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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