DEFB4A

Chr 8

defensin beta 4A

Also known as: BD-2, DEFB-2, DEFB102, DEFB2, DEFB4, HBD-2, SAP1

Defensins form a family of microbicidal and cytotoxic peptides made by neutrophils. Members of the defensin family are highly similar in protein sequence. This gene encodes defensin, beta 4, an antibiotic peptide which is locally regulated by inflammation. [provided by RefSeq, Jul 2008]

0
Active trials
28
Pathogenic / LP
104
ClinVar variants
12
Pubs (1 yr)
-0.6
Missense Z
1.97
LOEUF
Clinical SummaryDEFB4A
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
28 Pathogenic / Likely Pathogenic of 104 total submissions
Some data sources returned errors (1)

pubtator: Error: PubTator3 HTTP 502

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.97LOEUF
pLI 0.001
Z-score -2.95
OE 5.18 (0.831.97)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.63Z-score
OE missense 1.63 (1.011.95)
13 obs / 8.0 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE5.18 (0.831.97)
00.351.4
Missense OE1.63 (1.011.95)
00.61.4
Synonymous OE0.64
01.21.6
LoF obs/exp: 3 / 0.6Missense obs/exp: 13 / 8.0Syn Z: 0.49

ClinVar Variant Classifications

104 submitted variants in ClinVar

Classification Summary

Pathogenic28
Benign75
Conflicting1
28
Pathogenic
75
Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
28
Likely Pathogenic
0
VUS
0
Likely Benign
0
Benign
75
Conflicting
1
Total104

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

DEFB4A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

Search ClinicalTrials.gov →
Clinical Literature
Landmark / reviewRecent case evidence