DEFB105A

Chr 8

defensin beta 105A

Also known as: BD-5, DEFB-5, DEFB105

Defensins form a family of antimicrobial and cytotoxic peptides made by neutrophils. Defensins are short, processed peptide molecules that are classified by structure into three groups: alpha-defensins, beta-defensins and theta-defensins. All beta-defensin genes are densely clustered in four to five syntenic chromosomal regions. Chromosome 8p23 contains at least two copies of the duplicated beta-defensin cluster. This duplication results in two identical copies of defensin, beta 105, DEFB105A and DEFB105B, in tail-to-tail orientation. This gene, DEFB105A, represents the more centromeric copy. [provided by RefSeq, Oct 2014]

0
Active trials
88
Pathogenic / LP
213
ClinVar variants
0
Pubs (1 yr)
-0.4
Missense Z
1.76
LOEUF
Clinical SummaryDEFB105A
Population Constraint (gnomAD)
Constrained for loss-of-function variants (OE-LoF 0.00) despite low pLI — interpret in context.
📋
ClinVar Variants
88 Pathogenic / Likely Pathogenic· 7 VUS of 213 total submissions
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Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.76LOEUF
pLI 0.377
Z-score 0.86
OE 0.00 (0.001.76)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.36Z-score
OE missense 1.30 (0.861.85)
15 obs / 11.5 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.00 (0.001.76)
00.351.4
Missense OE1.30 (0.861.85)
00.61.4
Synonymous OE1.59
01.21.6
LoF obs/exp: 0 / 0.9Missense obs/exp: 15 / 11.5Syn Z: -0.90

ClinVar Variant Classifications

213 submitted variants in ClinVar

Classification Summary

Pathogenic85
Likely Pathogenic3
VUS7
Likely Benign2
Benign115
Conflicting1
85
Pathogenic
3
Likely Pathogenic
7
VUS
2
Likely Benign
115
Benign
1
Conflicting

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories· variant type breakdown unavailable

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
85
Likely Pathogenic
3
VUS
7
Likely Benign
2
Benign
115
Conflicting
1
Total213

Counts from ClinVar esearch · Updated hourly

View in ClinVar →

DEFB105A · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
Landmark / reviewRecent case evidence
Key Publications
Landmark & review papers · by relevance
PubMed
Top 1 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found