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DEE85

Chr XXLD

structural maintenance of chromosomes 1A

Also known as: CDLS2, DEE85, DXS423E, EIEE85, SB1.8, SMC1, SMC1L1, SMC1alpha

The encoded protein is a structural maintenance of chromosomes (SMC) protein that forms part of the cohesin multiprotein complex required for sister chromatid cohesion during cell division and functions in DNA repair through interactions with BRCA1. Mutations cause developmental and epileptic encephalopathy 85, which may include midline brain defects and represents an early-onset seizure disorder with developmental impairment. This condition follows X-linked dominant inheritance.

OMIMResearchSummary from RefSeq, OMIM
XLD1 OMIM phenotype
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/DEE85?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

DEE85 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

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Clinical Literature
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Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

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