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DEE2

Chr XXLD

cyclin dependent kinase like 5

Also known as: CFAP247, DEE2, EIEE2, ISSX, STK9

This protein kinase phosphorylates proteins and regulates cellular signaling pathways. Mutations cause developmental and epileptic encephalopathy 2, an X-linked dominant condition that can present as infantile spasm syndrome (West syndrome) with early onset seizures and developmental delays. The gene primarily affects neurological development and seizure control.

OMIMResearchSummary from RefSeq, OMIM
XLD1 OMIM phenotype
Clinical SummaryDEE2
💊
Clinical Trials
8 active or recruiting trials — potential therapeutic options may be available
Some data sources returned errors (2)

ensembl: Error: Ensembl fetch failed: 400 for https://rest.ensembl.org/lookup/symbol/homo_sapiens/DEE2?content-type=application/json&expand=1

gnomad: Error: Gene not found

Population Genetics & Constraint

Constraint data not available from gnomAD.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

DEE2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

CDKL5CDKL5 Deficiency DisorderCDD

International CDKL5 Clinical Research Network

RECRUITING
NCT05558371University of Colorado, DenverStarted 2021-02-15
No intervention.
Dravet Syndrome

Longitudinal Study of Phenotypic and Developmental Severity in Patients With Dravet Syndrome With SCN1A Gene Mutation

RECRUITING
NCT07251673Assistance Publique - Hôpitaux de ParisStarted 2025-09-15
Dravet Syndrome

A Clinical Study to Evaluate the Safety and Efficacy of ETX101 in Infants and Children With SCN1A-Positive Dravet Syndrome

RECRUITING
NCT05419492Phase PHASE1, PHASE2Encoded TherapeuticsStarted 2024-05-14
ETX101
Dravet SyndromeEpilepsy

Neurodevelopmental Impact of Epilepsy on Autonomic Function in Dravet Syndrome

ACTIVE NOT RECRUITING
NCT05472389Phase NAHospices Civils de LyonStarted 2022-10-14
Video-electroencephalographyBlood Samples
Dravet Syndrome

A Clinical Study to Evaluate the Safety and Efficacy of ETX101, an AAV9-Delivered Gene Therapy in Children With SCN1A-positive Dravet Syndrome (Australia Only)

ACTIVE NOT RECRUITING
NCT06112275Phase PHASE1, PHASE2Encoded TherapeuticsStarted 2024-02-28
ETX101
Dravet Syndrome

A Clinical Study to Evaluate the Safety and Efficacy of ETX101, an AAV9-Delivered Gene Therapy in Children With SCN1A-positive Dravet Syndrome

ACTIVE NOT RECRUITING
NCT06283212Phase PHASE1, PHASE2Encoded TherapeuticsStarted 2024-05-09
ETX101
EpilepsyDravet SyndromeDrug Resistant Epilepsy

A PET-MRI Study of Serotoninergic Brainstem Pathway in Patients With Dravet Syndrome

RECRUITING
NCT07013331Phase NAHospices Civils de LyonStarted 2026-05-04
[18F]MPPF PET-MRI
Dravet Syndrome

EXploring novEl Molecular Determinants of DRAvet Syndrome Phenotype Heterogeneity

ENROLLING BY INVITATION
NCT06371794Phase NAFondazione Policlinico Universitario Agostino Gemelli IRCCSStarted 2023-07-06
skin punch biopsy
Clinical Literature
Open Research Assistant →
Key Publications
Landmark & review papers · by relevance
PubMed
Top 2 results · since 2015Search PubMed ↗
Recent Gene-Specific Literature
Gene in title · MEDLINE · newest first
Europe PMC

No open access results found