DDX60

Chr 4

DExD/H-box helicase 60

DEAD box proteins, characterized by the conserved motif Asp-Glu-Ala-Asp (DEAD), are putative RNA helicases which are implicated in a number of cellular procsses involving RNA binding and alteration of RNA secondary structure. This gene encodes a DEXD/H box RNA helicase that functions as an antiviral factor and promotes RIG-I-like receptor-mediated signaling. [provided by RefSeq, Apr 2017]

0
Active trials
18
Pubs (1 yr)
52
P/LP submissions
0%
P/LP missense
0.59
LOEUF
DN
Mechanism· predicted
Clinical SummaryDDX60
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
52 unique Pathogenic / Likely Pathogenic· 182 VUS of 301 total submissions

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Moderate LoF intolerance
LoF Constraint
0.59LOEUF
pLI 0.000
Z-score 4.88
OE 0.45 (0.350.59)
Moderately constrained

More LoF-intolerant than ~75% of genes

Missense Constraint
1.25Z-score
OE missense 0.88 (0.830.93)
750 obs / 853.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.45 (0.350.59)
00.351.4
Missense OE0.88 (0.830.93)
00.61.4
Synonymous OE0.98
01.21.6
LoF obs/exp: 42 / 92.6Missense obs/exp: 750 / 853.1Syn Z: 0.32
DN
0.6646th %ile
GOF
0.4382th %ile
LOF
0.2968th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

301 submitted variants in ClinVar

Classification Summary

Pathogenic49
Likely Pathogenic3
VUS182
Likely Benign24
Benign3
49
Pathogenic
3
Likely Pathogenic
182
VUS
24
Likely Benign
3
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
49
0
49
Likely Pathogenic
0
0
3
0
3
VUS
0
172
10
0
182
Likely Benign
0
22
0
2
24
Benign
0
2
1
0
3
Total0196632261

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

DDX60 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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