CYP4Z1

Chr 1

cytochrome P450 family 4 subfamily Z member 1

Also known as: CYP4A20

This enzyme catalyzes the hydroxylation and epoxidation of fatty acids, particularly lauric and myristic acids, and produces epoxyeicosatrienoic acid from arachidonic acid. CYP4Z1 mutations have not been established as a cause of human disease, and no clear inheritance pattern or clinical phenotype has been defined for this gene. The gene shows tolerance to loss-of-function variants (LOEUF 1.464), suggesting that complete loss of this enzyme may not cause severe developmental phenotypes.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 1.46
Clinical SummaryCYP4Z1
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.46LOEUF
pLI 0.000
Z-score -0.22
OE 1.05 (0.761.46)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.11Z-score
OE missense 0.98 (0.891.09)
260 obs / 265.1 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE1.05 (0.761.46)
00.351.4
Missense OE0.98 (0.891.09)
00.61.4
Synonymous OE0.85
01.21.6
LoF obs/exp: 25 / 23.8Missense obs/exp: 260 / 265.1Syn Z: 1.11
DN
0.6744th %ile
GOF
0.5367th %ile
LOF
0.3455th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CYP4Z1 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Full-Text Mentions
NLP-detected gene mentions in article bodies · via PubTator3
PubTator3
Top 5 full-text resultsSearch PubTator3 ↗