CYP2J2

Chr 1

cytochrome P450 family 2 subfamily J member 2

Also known as: CPJ2, CYPIIJ2

This gene encodes a cytochrome P450 monooxygenase that catalyzes the epoxidation of arachidonic acid and other polyunsaturated fatty acids in cardiac tissue, producing epoxyeicosatrienoic acids that have cardiovascular effects. The gene shows low constraint against loss-of-function variants (LOEUF 1.39), and no established Mendelian diseases have been definitively linked to CYP2J2 mutations in the pediatric population. While variants in this gene have been studied in relation to cardiovascular phenotypes, clear disease associations with defined inheritance patterns remain to be established.

OMIMResearchSummary from RefSeq, UniProt
DNmechanismLOEUF 1.39
Clinical SummaryCYP2J2
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.39LOEUF
pLI 0.000
Z-score 0.08
OE 0.98 (0.701.39)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.14Z-score
OE missense 0.98 (0.881.08)
270 obs / 276.4 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.98 (0.701.39)
00.351.4
Missense OE0.98 (0.881.08)
00.61.4
Synonymous OE0.93
01.21.6
LoF obs/exp: 23 / 23.4Missense obs/exp: 270 / 276.4Syn Z: 0.55
DN
0.6840th %ile
GOF
0.5465th %ile
LOF
0.3549th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CYP2J2 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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Clinical Literature
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Key Publications
Landmark & review papers · by relevance
PubMed
Top 5 results · since 2015Search PubMed ↗