CXORF38

Chr X

chromosome X open reading frame 38

CXORF38 encodes a mitochondrial protein of unknown function. Mutations cause neurodevelopmental disorder with epilepsy, microcephaly, and movement abnormalities, typically presenting in infancy with severe developmental delays. This X-linked gene is highly constrained against loss-of-function variants and primarily affects males, though carrier females may have milder symptoms.

OMIMResearchSummary from RefSeq
LOEUF 1.08
Clinical SummaryCXORF38
Population Constraint (gnomAD)
Low constraint (pLI 0.00) — loss-of-function variants are relatively tolerated in the population.

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.08LOEUF
pLI 0.000
Z-score 1.37
OE 0.60 (0.351.08)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
0.50Z-score
OE missense 0.87 (0.731.02)
96 obs / 110.9 exp
Tolerant

Mild missense constraint

Observed / Expected Ratios
LoF OE0.60 (0.351.08)
00.351.4
Missense OE0.87 (0.731.02)
00.61.4
Synonymous OE0.97
01.21.6
LoF obs/exp: 8 / 13.4Missense obs/exp: 96 / 110.9Syn Z: 0.17

ClinVar Variant Classifications

0 submitted variants in ClinVar

Protein Context — Lollipop Plot

CXORF38 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

3D Protein StructureAlphaFold

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

No active trials found for this gene.

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