CXCL12

Chr 10

C-X-C motif chemokine ligand 12

Also known as: IRH, PBSF, SCYB12, SDF1, TLSF, TPAR1

The encoded protein is a chemokine that functions as a chemoattractant for T-lymphocytes and monocytes, activating the CXCR4 receptor to induce calcium mobilization and cell migration, and playing critical roles in immune cell trafficking, embryonic development, and B-cell lymphopoiesis. Mutations in this gene are associated with resistance to HIV-1 infection. The gene shows relatively low constraint to loss-of-function variation (pLI 0.12, LOEUF 1.18), suggesting tolerance to protein-truncating variants.

Summary from RefSeq, OMIM, UniProt
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Primary Disease Associations & Inheritance

{AIDS, resistance to}MIM #609423
7
Active trials
574
Pubs (1 yr)
13
P/LP submissions
0%
P/LP missense
1.18
LOEUF
DN
Mechanism· predicted
Clinical SummaryCXCL12
Population Constraint (gnomAD)
Low constraint (pLI 0.12) — loss-of-function variants are relatively tolerated in the population.
📋
ClinVar Variants
13 unique Pathogenic / Likely Pathogenic· 22 VUS of 71 total submissions
💊
Clinical Trials
7 active or recruiting trials — potential therapeutic options may be available

Population Genetics & Constraint

gnomAD v4 — loss-of-function & missense intolerance

Tolerant — LoF & missense variants common in population
LoF Constraint
1.18LOEUF
pLI 0.119
Z-score 1.33
OE 0.38 (0.151.18)
Tolerant

Highly tolerant — LoF variants common in population

Missense Constraint
-0.25Z-score
OE missense 1.08 (0.911.29)
87 obs / 80.6 exp
Tolerant

Tolerant to missense variation

Observed / Expected Ratios
LoF OE0.38 (0.151.18)
00.351.4
Missense OE1.08 (0.911.29)
00.61.4
Synonymous OE0.96
01.21.6
LoF obs/exp: 2 / 5.3Missense obs/exp: 87 / 80.6Syn Z: 0.16
DN
0.77top 25%
GOF
0.4382th %ile
LOF
0.2484th %ile

The highest-scoring mechanism for this gene is dominant-negative.

DNprediction above median

Note: In-silico variant effect predictors (SIFT, PolyPhen, REVEL, CADD) may underestimate pathogenicity of missense variants in genes with GOF or DN mechanisms. Consider functional evidence and clinical context.

Predictions from Badonyi M, Marsh JA. PLoS ONE. 2024;19(8):e0307312.

ClinVar Variant Classifications

71 submitted variants in ClinVar

Classification Summary

Pathogenic11
Likely Pathogenic2
VUS22
Likely Benign6
Benign25
11
Pathogenic
2
Likely Pathogenic
22
VUS
6
Likely Benign
25
Benign

Curated Variants Distribution

Classified variants from ClinVar · 5 ACMG categories

ClassificationLoFMissense + InframeNon-codingSynonymousTotal
Pathogenic
0
0
11
0
11
Likely Pathogenic
0
0
2
0
2
VUS
0
20
2
0
22
Likely Benign
0
1
2
3
6
Benign
0
0
24
1
25
Total02141466

LoF = frameshift, stop gained/lost, canonical splice · Counts from ClinVar esearch · Updated hourly

View in ClinVar →

Protein Context — Lollipop Plot

CXCL12 · protein map & ClinVar variants

Showing all ClinVar variants across the protein. Search a specific variant to highlight its position.

Clinical Trials

Active and recruiting trials from ClinicalTrials.gov

Diabetic Kidney Disease

Role of Finerenone in African American Veterans With Diabetic Kidney Disease

NOT YET RECRUITING
NCT07155694Phase PHASE4Washington D.C. Veterans Affairs Medical CenterStarted 2025-09
Finerenone 10 MGEmpagliflozin 10 MG
High-Risk CancerLocally Advanced Breast Cancer

Three Fraction Radiation to Induce Immuno-Oncologic Response

ACTIVE NOT RECRUITING
NCT03978663Phase NALondon Health Sciences Centre Research Institute OR Lawson Research Institute of St. Joseph'sStarted 2020-09-02
Neoadjuvant radiotherapy
Acute-On-Chronic Liver FailureAlcoholic HepatitisLiver Cirrhosis, Alcoholic

A-TANGO Phase 2 Study

NOT YET RECRUITING
NCT06890039Phase PHASE2Yaqrit LtdStarted 2025-09-01
PlaceboTAK-242G-CSF (Filgrastim)
Waldenstrom's DiseaseWaldenstrom Macroglobulinemia

Prognostic Value of Circulating Tumoral DNA After the First 6 Months of Treatment in Patients With Waldenström Macroglobulinemia

RECRUITING
NCT04893564Phase NACentre Hospitalier Universitaire, AmiensStarted 2022-05-16
bone marrow sampleblood sample
Mesothelioma

New Preclinical and Clinical Approaches to Mesothelioma

RECRUITING
NCT06536179Marco Emilio BianchiStarted 2024-07-25
Gastric and Cardia Adenocarcinomas

Biomoleculars Markers of Sensitivity to Pre- and Post-operative Chemotherapy of Gastric and Cardia Adenocarcinomas: a Pilot Study

RECRUITING
NCT02491840Phase NAUniversity Hospital, Strasbourg, FranceStarted 2016-05
Biopsy
Idiopathic Intracranial Hypertension

Biomarkers in the Etiology of Idiopathic Intracranial Hypertension

RECRUITING
NCT06059703Phase NAUniversity Hospital, MontpellierStarted 2023-11-27
Blood punctionCentral blood samplingIntracranial pressure measurement
Clinical Literature
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